An Uncommon Presentation of Klippel-Trenaunay Syndrome Presenting with Acute Hip Pain

Introduction: Klippel-Trenaunay syndrome (KTS) is a syndrome that affects the development of blood vessels, soft tissues and bones. We report a rare case of KTS presenting with spontaneous acute hip pain.

Case Presentation: A 38-year-old male patient presented to the emergency department with a complaint of right hip pain and elevated temperature of one moth duration. These symptoms disappeared spontaneously after two days of hospitalization. Computerized tomography (CT) scan revealed a common iliac vein hypoplasia and collateral circulation associated with asymmetric psoas muscles. A diagnosis of KTS was made based on the vascular abnormalities and associated soft tissue changes.

Conclusion: Our case illustrates a new case of KTS presenting with spontaneous acute hip pain.